Одеський національний медичний університет, Одеса, Україна
DOI 10.32782/2226-2008-2025-6-11
Актуальність. Однією з найчастіших вроджених аномалій у світі є вроджені вади серця (ВВС), які завдають шкоди здоров’ю людини, призводять до інвалідизації і є основною причиною летальності немовлят.
Мета – узагальнення глобальної поширеності ВВС серед живонароджених дітей та тенденцій щодо поліпшення діагностики та лікування у світі. Під «тенденціями» розуміли часові зміни зареєстрованої частоти ВВС та показників смертності, які залежать від системи – організації скринінгу, реєстрації випадків і доступності лікування.
Результат. Частота ВВС у світі коливається в межах 8–12‰. За структурою найпоширенішими дефектами є: VSD (40%), ASD (14%), PDA (10%), PS (7,6%), TOF (5,5%), CoA (4,7%), TGA (3,7%), HLHS (2,6%). За умови своєчасної хірургічної допомоги 95% дітей виживають. В Україні щороку народжується близько 4500 дітей із ВВС, з яких приблизно 30–40% потребують хірургічного втручання у перший рік життя.
Ключові слова: вроджені вади серця, діти, стан проблеми, виклики системи.
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