№ 4 (189) 2024 р. С. 62–71

СИНДРОМ ПОДОВЖЕНОГО ІНТЕРВАЛУ QT У ПРАКТИЦІ ПЕДІАТРА

Г. С. Сенаторова, О. В. Омельченко, І. М. Галдіна, О. В. Бучнева

Харківський національний медичний університет, Харків, Україна
Комунальне некомерційне підприємство Харківської обласної ради «Обласна дитяча клінічна лікарня», Харків, Україна
ДУ «Інститут загальної та невідкладної хірургії імені В. Т. Зайцева Національної академії медичних наук України», Харків, Україна

DOI 10.32782/2226-2008-2024-4-11

Мета роботи – представити сучасний погляд на проблему синдрому подовженого інтервалу QT (LQTS) у дітей, що дозволить своєчасно попереджувати розвиток раптової серцевої смерті в дитячому віці та проілюструвати тактику ведення хворого з LQTS власним клінічним спостереженням.

У роботі наведено огляд сучасної літератури щодо причин та механізмів розвитку, діагностики та лікування LQTS у дітей. Представлено власне клінічне спостереження підлітка з LQTS та тактику його ведення.

Викладені матеріали дозволять розширити знання лікарів-педіатрів про LQTS як предиктора фатальних порушень ритму серця у дітей та дадуть можливість своєчасно попереджувати розвиток раптової серцевої смерті в дитячому віці.

Ключові слова: синдром подовженого інтервалу QT, синдром раптової cерцевої смерті, каналопатії, тахікардія типу «пірует», діти.

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