The purpose of our study was to determine the reliability of echocardiography (ECHO) in the diagnosis of 26 patients with pulmonary atresia (PA) with ventricular septal defects (VSD) for estimation of anatomy and degree of hemodynamics disturbances of this anomaly for determination of indications to operative treatment. We performed two-dimensional ECHO, continuous wave Doppler examination and color Doppler mapping of the right ventricle outflow tract and all visible structures of the pulmonary artery. ECHO is the informative method for preoperative diagnostics of PAA with VSD and determination its type. On the basis of ECHO we determined indications to urgent surgical intervention in newborns with PAA type «А», when patients have truncus and branches of pulmonary artery and lungs supply with blood only through PDA (patent ductus arteriosus).
