The article presents experience of palliative procedures application for formation of the arterial pulmonary bed with further complete repair (CR) of the pulmonary atresia (PA) with ventricular septal defect (VSD). In the National Institute of Cardiovascular Surgery named after N. Amosov 161 patient of the age from 3 days to 228 months have been followed up within 1982 to 2009. CR was performed in 87 patients, primary — only in 6 (3.7%), the rest 81 (50.3%) after palliative procedures. During CR transannular patch was performed in 35 (40.2%), 25 (28.7%) with a monocusp method Loma Linda MC CA, 27 (31.1%) had conduit implantation. Hospital mortality after CR for the last 6 years was 5.5%.
